Congenital Simple Hamartoma of the RPE (CSHRPE)

Fundus photograph (1), green free (2) and red free (3) images

Fundus photos show a circular dark pigmented lesion with distinct borders superior to the right fovea. It is visible on both the green-free and red-free images.

Stereoscopic image of the CSHRPE

Please use a stereoviewer or 15 prism dioptres base out to view the image.

The elevated nature of this pigmented lesion can be visualised on stereoscopic view.

Fundus autofluorescence image

FAF imaging shows corresponding hypo-autofluorescence. There is also a slight disturbance of the autofluorescent signal at the central macula.

Spectralis OCT line scan through the lesion

OCT line scans shows a focal region of hyper-reflectivity within the inner retina, protruding into the vitreous. The margins are clear-cut and there is posterior optical shadowing.

Spectralis OCT volume scan through the lesion

OCT line scans shows a focal region of hyper-reflectivity within the inner retina, protruding into the vitreous. The margins are clear-cut and there is posterior optical shadowing.

In the OCT line scan through fovea, there is a slight disruption of the RPE, ellipsoid zone and outer retinal layer.

There are no signs of vitreoretinal traction or exudative changes.

Fundus photograph (1), green free (2) and red free (3) images

Fundus photos show a darkly pigmented lesion with a small region of internal hypopigmentation superotemporal to the right fovea. It displays mild elevation on funduscopic examination.

It is visible on both the green-free and red-free images.

Fundus autofluorescence image

FAF imaging shows corresponding hypo-autofluorescence

Fundus photograph (1), green free (2) and red free (3) images

Fundus photos show a small, darkly pigmented lesion at the superonasal macula of the left eye. It exhibits sharps borders and is visible on both the green-free and red-free image.

Stereoscopic image of the lesion

Please use a stereoviewer or 15 prism dioptres base out to view the image.

Stereoscopic examination highlights the slight elevation associated with pigmented finding.

Fundus autoflurescence image

FAF imaging shows corresponding hypo-autofluorescence

Spectralis OCT line scan through the lesion

OCT line scans shows that the lesion is located in the nerve fibre layer with slight protrusion in the vitreous. There also optical shadowing posteriorly. The adjacent retina appears unremarkable with no signs of vitreomacular traction or exudative changes.

Spectralis OCT volume scan through the lesion

OCT line scans shows that the lesion is located in the nerve fibre layer with slight protrusion in the vitreous. There also optical shadowing posteriorly. The adjacent retina appears unremarkable with no signs of vitreomacular traction or exudative changes.