Overview

Pachychoroid neovasculopathy (PNV) is characterised by the presence of type 1 choroidal neovascularization overlying pachychoroid disease changes. It is thought to develop secondary to pachychoroid pigment epitheliopathy (PPE) or central serous chorioretinopathy (CSCR) and can progress to polypoidal choroidal vasculopathy (PCV) with the development of polypoidal lesions.

PCV may be associated with blur and/or metamorphopsia.

Colour fundus photographs usually show mild pigmentary changes at the macula.

OCT imaging typically shows a shallow irregular PED, also known as the double-layer sign. The sign is characterized by two hyper-reflective bands, where the upper band represents the RPE and the lower band represents Bruch’s membrane. The material residing in between these two hyper-reflective layers may represent choroidal neovascularization.

OCT angiography shows a tangled network of flow signal that coincides with the double-layer sign on structural OCT scans.

Case Examples

Differential Diagnosis

References

Borooah, S, Sim, P.Y, Phatak, S, Moraes, G, Wu, C.Y, Cheung, CMG., Pal, B, Bujarborua, D. (2020), Pachychoroid spectrum disease. Acta Ophthalmol.

Cheung, CMG, Lee, WK, Koizumi, H. et al. Pachychoroid disease. Eye 33, 14–33 (2019).